Systemic Cardiac Amyloidoses
University of Ferrara · University of Pavia · +2 more institutions
Abstract
BACKGROUND: Most studies of amyloidotic cardiomyopathy consider as a single entity the 3 main systemic cardiac amyloidoses: acquired monoclonal immunoglobulin light-chain (AL); hereditary, mutated transthyretin-related (ATTRm); and wild-type transthyretin-related (ATTRwt). In this study, we compared the diagnostic/clinical profiles of these 3 types of systemic cardiac amyloidosis. METHODS AND RESULTS: We conducted a longitudinal study of 233 patients with clear-cut diagnosis by type of cardiac amyloidosis (AL, n=157; ATTRm, n=61; ATTRwt, n=15) at 2 large Italian centers providing coordinated amyloidosis diagnosis/management facilities since 1990. Average age at diagnosis was higher in AL than in ATTRm…
Citation impact
- FWCI
- 9.72
- Percentile
- 100%
- References
- 33
Authors
24- CRClaudio RapezziCorresponding
University of Ferrara, University of Pavia, University Hospital Foundation, Ospedale Bellaria
- GMGiampaolo Merlini
University of Ferrara, University of Pavia, University Hospital Foundation, Ospedale Bellaria
- CCCandida Cristina Quarta
University of Ferrara, University of Pavia, University Hospital Foundation, Ospedale Bellaria
- LRLetizia Riva
University of Ferrara, University of Pavia, University Hospital Foundation, Ospedale Bellaria
- SLSimone Longhi
University of Ferrara, University of Pavia, University Hospital Foundation, Ospedale Bellaria
Topics & keywords
- Medicine
- Intensive care medicine
- Cardiology
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