Origins of Cystic Fibrosis Lung Disease
University of Iowa · Howard Hughes Medical Institute
Indexed incrossrefpubmed
Abstract
Mutations in the gene encoding the cystic fibrosis transmembrane conductance regulator undermine many host defense systems by inhibiting the function of airway-surface liquid, causing flaws in mucociliary transport, and compromising other lung-protection mechanisms.
Citation impact
661
total citations
- FWCI
- 54.15
- Percentile
- 100%
- References
- 79
Citations per year
Authors
3Topics & keywords
Topics
Keywords
- Cystic fibrosis
- Cystic fibrosis transmembrane conductance regulator
- Medicine
- Lung
- Mucociliary clearance
- Lung function
- Lung disease
- Regulator
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