Survival in incident and prevalent cohorts of patients with pulmonary arterial hypertension

Pulmonary arterial hypertension (PAH) is a progressive, fatal disease. We studied 674 consecutive adult patients who were prospectively enrolled in the French PAH registry (121 incident and 553 prevalent cases). Two survival analyses were performed. First, the cohort of 674 patients was followed for 3 yrs after study entry and survival rates described. Then, we focused on the subset with incident idiopathic, familial and anorexigen-associated PAH (n = 56) combined with prevalent patients who were diagnosed

• IN
  Institut National de la Santé et de la Recherche Médicale
• AP
  Actelion Pharmaceuticals