articleJournal of Clinical InvestigationMar 3, 2014BRONZE OA

Fibrotic extracellular matrix activates a profibrotic positive feedback loop

Twin Cities Orthopedics · University of Minnesota · +3 more institutions

PubMed
Indexed incrossrefdoajpubmed

Abstract

Pathological remodeling of the extracellular matrix (ECM) by fibroblasts leads to organ failure. Development of idiopathic pulmonary fibrosis (IPF) is characterized by a progressive fibrotic scarring in the lung that ultimately leads to asphyxiation; however, the cascade of events that promote IPF are not well defined. Here, we examined how the interplay between the ECM and fibroblasts affects both the transcriptome and translatome by culturing primary fibroblasts generated from IPF patient lung tissue or nonfibrotic lung tissue on decellularized lung ECM from either IPF or control patients. Surprisingly, the origin of the ECM had a greater impact on gene expression than did cell origin, and differences in…

No related works found for this paper.

Funding