Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease
University of Göttingen · Western General Hospital · +21 more institutions
Abstract
Several molecular subtypes of sporadic Creutzfeldt-Jakob disease have been identified and electroencephalogram and cerebrospinal fluid biomarkers have been reported to support clinical diagnosis but with variable utility according to subtype. In recent years, a series of publications have demonstrated a potentially important role for magnetic resonance imaging in the pre-mortem diagnosis of sporadic Creutzfeldt-Jakob disease. Magnetic resonance imaging signal alterations correlate with distinct sporadic Creutzfeldt-Jakob disease molecular subtypes and thus might contribute to the earlier identification of the whole spectrum of sporadic Creutzfeldt-Jakob disease cases. This multi-centre international study…
Citation impact
- FWCI
- 17.79
- Percentile
- 100%
- References
- 39
Authors
27- IZInga ZerrCorresponding
- KKKai Kallenberg
University of Göttingen
- DSDavid Summers
Western General Hospital, University of Edinburgh
- CRCarlos Romero
Fundación para la Lucha contra las Enfermedades Neurológicas de la Infancia, Instituto de Neurología de Buenos Aires
- ATA.L. Taratuto
Fundación para la Lucha contra las Enfermedades Neurológicas de la Infancia, Instituto de Neurología de Buenos Aires
Topics & keywords
- Magnetic resonance imaging
- Differential diagnosis
- Putamen
- Medicine
- Pathology
- Disease
- Cerebrospinal fluid
- Dementia
- Partnerships for the goals
Funding
- ECEuropean Commission
- ECEuropean Centre for Disease Prevention and Control
- BFBundesamt für Gesundheit
- BFBundesministerium für Bildung und Forschung
- MDMinisterio de Ciencia, Tecnología e Innovación Productiva
- BFBundesministerium für GesundheitAwards: 1369-341, grant no 1369-341
- MDMinisterio de Salud de la Nación
- FFleni
- RKRobert Koch Institut