Left Cardiac Sympathetic Denervation in the Management of High-Risk Patients Affected by the Long-QT Syndrome
University of Helsinki · Peking University · +10 more institutions
Abstract
BACKGROUND: The management of long-QT syndrome (LQTS) patients who continue to have cardiac events (CEs) despite beta-blockers is complex. We assessed the long-term efficacy of left cardiac sympathetic denervation (LCSD) in a group of high-risk patients. METHODS AND RESULTS: We identified 147 LQTS patients who underwent LCSD. Their QT interval was very prolonged (QTc, 543+/-65 ms); 99% were symptomatic; 48% had a cardiac arrest; and 75% of those treated with beta-blockers remained symptomatic. The average follow-up periods between first CE and LCSD and post-LCSD were 4.6 and 7.8 years, respectively. After LCSD, 46% remained asymptomatic. Syncope occurred in 31%, aborted cardiac arrest in 16%, and sudden death…
Citation impact
- FWCI
- 13.54
- Percentile
- 100%
- References
- 25
Authors
18- PJPeter J. SchwartzCorresponding
University of Helsinki, Peking University, University of Pavia, Stellenbosch University, Tygerberg Hospital, University of Alabama at Birmingham, Fondazione Salvatore Maugeri, Peking University People's Hospital, Policlinico San Matteo Fondazione, Istituti di Ricovero e Cura a Carattere Scientifico
- SGSilvia G. Priori
University of Helsinki, Peking University, University of Pavia, Stellenbosch University, Tygerberg Hospital, University of Alabama at Birmingham, Fondazione Salvatore Maugeri, Peking University People's Hospital, Policlinico San Matteo Fondazione, Istituti di Ricovero e Cura a Carattere Scientifico
- MCMarina Cerrone
University of Helsinki, Peking University, University of Pavia, Stellenbosch University, Tygerberg Hospital, University of Alabama at Birmingham, Fondazione Salvatore Maugeri, Peking University People's Hospital, Policlinico San Matteo Fondazione, Istituti di Ricovero e Cura a Carattere Scientifico
- CSCarla Spazzolini
University of Helsinki, Peking University, University of Pavia, Stellenbosch University, Tygerberg Hospital, University of Alabama at Birmingham, Fondazione Salvatore Maugeri, Peking University People's Hospital, Policlinico San Matteo Fondazione, Istituti di Ricovero e Cura a Carattere Scientifico
- AOAttilio Odero
University of Helsinki, Peking University, University of Pavia, Stellenbosch University, Tygerberg Hospital, University of Alabama at Birmingham, Fondazione Salvatore Maugeri, Peking University People's Hospital, Policlinico San Matteo Fondazione, Istituti di Ricovero e Cura a Carattere Scientifico
Topics & keywords
- Medicine
- Long QT syndrome
- QT interval
- Sympathetic Denervation
- Cardiology
- Internal medicine
- Asymptomatic
- Sudden cardiac death
- Good health and well-being