Risk assessment, prognosis and guideline implementation in pulmonary arterial hypertension
Université Paris-Sud · Inserm · +23 more institutions
Abstract
Current European guidelines recommend periodic risk assessment for patients with pulmonary arterial hypertension (PAH). The aim of our study was to determine the association between the number of low-risk criteria achieved within 1 year of diagnosis and long-term prognosis. Incident patients with idiopathic, heritable and drug-induced PAH between 2006 and 2016 were analysed. The number of low-risk criteria present at diagnosis and at first re-evaluation were assessed: World Health Organization (WHO)/New York Heart Association (NYHA) functional class I or II, 6-min walking distance (6MWD) >440 m, right atrial pressure <8 mmHg and cardiac index ≥2.5 L·min −1 ·m −2 . 1017 patients were included (mean age 57…
Citation impact
- FWCI
- 49.43
- Percentile
- 100%
- References
- 21
Authors
18- ABAthénaïs BouclyCorresponding
Université Paris-Sud, Inserm, Université Paris-Saclay, Assistance Publique – Hôpitaux de Paris, Hypertension pulmonaire : physiopathologie et innovation thérapeutique, Hôpital Marie Lannelongue, Bicêtre Hospital
- JWJason Weatherald
Inserm, University of Calgary, Assistance Publique – Hôpitaux de Paris, Hypertension pulmonaire : physiopathologie et innovation thérapeutique, Hôpital Marie Lannelongue, Bicêtre Hospital
- LSLaurent Savale
Université Paris-Sud, Inserm, Université Paris-Saclay, Assistance Publique – Hôpitaux de Paris, Hypertension pulmonaire : physiopathologie et innovation thérapeutique, Hôpital Marie Lannelongue, Bicêtre Hospital
- XJXavier Jaïs
Université Paris-Sud, Inserm, Université Paris-Saclay, Assistance Publique – Hôpitaux de Paris, Hypertension pulmonaire : physiopathologie et innovation thérapeutique, Hôpital Marie Lannelongue, Bicêtre Hospital
- VCVincent Cottin
Université Claude Bernard Lyon 1, Hospices Civils de Lyon, Hôpital Louis Pradel
Topics & keywords
- Medicine
- Guideline
- Intensive care medicine
- Cardiology
- Risk assessment
- Internal medicine
- Pathology
Funding
- EREuropean Respiratory Society
- CTCanadian Thoracic Society
- LTLloyd's Tercentenary Research Foundation
- ANAgence Nationale de la RechercheAwards: ANR-15-RHUS-0002, ANR-10, ANR-10-LABX-0033
- INInstitut National de la Santé et de la Recherche Médicale
- APAssistance Publique - Hôpitaux de Paris
- UPUniversité Paris-Sud
- APAssistance publique-Hôpitaux de Paris
- LDLaboratoire d'Excellence en Recherche sur le Médicament et l'Innovation ThérapeutiqueAward: ANR-10-LABX-0033