International League Against Epilepsy classification and definition of epilepsy syndromes with onset in childhood: Position paper by the ILAE Task Force on Nosology and Definitions

The 2017 International League Against Epilepsy classification has defined a three-tier system with epilepsy syndrome identification at the third level. Although a syndrome cannot be determined in all children with epilepsy, identification of a specific syndrome provides guidance on management and prognosis. In this paper, we describe the childhood onset epilepsy syndromes, most of which have both mandatory seizure type(s) and interictal electroencephalographic (EEG) features. Based on the 2017 Classification of Seizures and Epilepsies, some syndrome names have been updated using terms directly describing the seizure semiology. Epilepsy syndromes beginning in childhood have been divided into three categories:…

• UD
  U.S. Department of Defense

  Awards: W81XWH, W81XWH-18, W81XWH-18-1-0612
• NI
  National Institute for Health and Care Research
• ET
  Evelyn Trust
• NI
  National Institutes of Health

  Awards: U54 NS100064, NS100064, W81XWH, NS43209
• NC
  NIHR Cambridge Biomedical Research Centre